Congenital self-healing reticulohistiocytosis

Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

• Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
• Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.

History

It was first described by Ken Hashimoto and Martin S. Pritzker in 1973.

See also

• List of cutaneous conditions
• X-type histiocytosis

References